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KMID : 0357919850190020226
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Korean Journal of Pathology
1985 Volume.19 No. 2 p.226 ~ p.230
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Sturge-Weber Syndrome-Report of an incomplete form-
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김혜연/Hye Teon Kim
이갑노/백승룡/이기찬/임창수/남석호/지제근/Kap No Lee/Seung Young Paik/Ki Chan Lee/Chang Soo Lim/Suck Ho Nam/Je G. Chi
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Abstract
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The Sturge Weber syndrome is an uncommon disorder characterized by port-wine
nevus of the face with angiomatosis of the ipsilateral cerebral leptomeninges and
extensive calcification in the underlying cerebral cortex. Associated with this syndrome
are mental retardation, choroidal angioma, buphthalmus or glaucoma, seizure and
hemiplegia.
We studied a case of incomplete form of Sturage Weber syndrome in a 12year-old
boy, who had generalized seizure, a homonymous hemianopsia, intracranial calcification
and leptomeningeal angiomatosis. There are no characteristic facial nevus, mental
retardation, occular changes and hemiplegia.
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